Acute Megakaryoblastic Leukaemia (AML M7): Rare association of Down syndrome and Haemoglobin E-Beta Thalassaemia

نویسندگان

  • Gautam Kumar Mandal
  • Koushik Dewan
  • Manik Mondal
  • Rajarshi Basu
  • Himel Bera
چکیده

Acute megakaryoblastic leukemia(AML-M7) is a rare type of pediatric AML. It represents approximately 1% of all leukemias during childhood & has an incidence of 0.5% per million per year. In young children with Down syndrome, AML-M7 is the most common type of AML. There is no association reported till date in between Down syndrome & Haemoglobin E-Beta thalassaemia. In our case we got rare association of AML-M7 in a case of Down syndrome with Haemoglobin E-Beta thalassemia. This association may be incidental. But we are reporting this case for future review.

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تاریخ انتشار 2013